Anti-Recombinant-GBA antibody [RM1J43] (STJA0023433)

SPECIFICATIONS
ClonalityMonoclonal
HostRabbit
ConjugationUnconjugated
IsotypeIgG
STJA0023433
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General Information

Short DescriptionRabbit monoclonal anti-Recombinant-Lysosomal Acid Glucosylceramidase for use in IHC and WB in Human and Rat samples. Datasheet included with dilution recommendations, and related reagents.
ApplicationsIHC/WB
HostRabbit
ReactivityHuman/Rat
NoteSTRICTLY FOR FURTHER SCIENTIFIC RESEARCH USE ONLY (RUO). MUST NOT BE USED IN DIAGNOSTIC OR THERAPEUTIC APPLICATIONS.

Product Properties

ClonalityMonoclonal
Clone IDRM1J43
IsotypeIgG
ConjugationUnconjugated
PurificationProtein A/G purified from cell culture supernatant
Dilution RangeIHC: 1:100-1:200
Formulation0.01M PBS
Storage InstructionSuitable for storage at +4°C between 1-2 weeks. For longer term store at-20°C for up to 12 months.

Target Information

Gene SymbolGBA1
Gene ID2629
Uniprot IDGBA1_HUMAN

Additional Info

Protein Name Lysosomal Acid Glucosylceramidase
Lysosomal Acid Gcase
Acid Beta-Glucosidase
Alglucerase
Beta-Glucocerebrosidase
Beta-Gc
Beta-Glucosylceramidase 1
Cholesterol Glucosyltransferase
Sgtase
Cholesteryl-Beta-Glucosidase
D-Glucosyl-N-Acylsphingosine Glucohydrolase
Glucosylceramidase Beta 1
Imiglucerase
Lysosomal Cholesterol Glycosyltransferase
Lysosomal Galactosylceramidase
Lysosomal Glycosylceramidase
Database Links Reactome: R-HSA-390471
Reactome: R-HSA-9840310
Cellular Localisation Lysosome Membrane
Peripheral Membrane Protein
Lumenal Side
Interaction With Saposin-C Promotes Membrane Association
Targeting To Lysosomes Occurs Through An Alternative Mpr-Independent Mechanism Via Scarb2
Alternative Antibody Names Anti-Lysosomal Acid Glucosylceramidase antibody
Anti-Lysosomal Acid Gcase antibody
Anti-Acid Beta-Glucosidase antibody
Anti-Alglucerase antibody
Anti-Beta-Glucocerebrosidase antibody
Anti-Beta-Gc antibody
Anti-Beta-Glucosylceramidase 1 antibody
Anti-Cholesterol Glucosyltransferase antibody
Anti-Sgtase antibody
Anti-Cholesteryl-Beta-Glucosidase antibody
Anti-D-Glucosyl-N-Acylsphingosine Glucohydrolase antibody
Anti-Glucosylceramidase Beta 1 antibody
Anti-Imiglucerase antibody
Anti-Lysosomal Cholesterol Glycosyltransferase antibody
Anti-Lysosomal Galactosylceramidase antibody
Anti-Lysosomal Glycosylceramidase antibody
Anti-GBA1 antibody
Anti-GBA antibody
Anti-GC antibody
Anti-GLUC antibody

Information sourced from Uniprot.org

Citations

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