Function | Catalyzes the pyridoxal 5'-phosphate (PLP)-dependent condensation of succinyl-CoA and glycine to form aminolevulinic acid (ALA), with CoA and CO2 as by-products. |
Protein Name | 5-Aminolevulinate Synthase - Non-Specific - MitochondrialAlas-H5-Aminolevulinic Acid Synthase 1Delta-Ala Synthase 1Delta-Aminolevulinate Synthase 1 |
Database Links | Reactome: R-HSA-189451Reactome: R-HSA-1989781Reactome: R-HSA-2151201Reactome: R-HSA-9837999 |
Cellular Localisation | Mitochondrion Inner MembranePeripheral Membrane ProteinLocalizes To The Matrix Side Of The Mitochondrion Inner Membrane |
Alternative Protein Names | 5-Aminolevulinate Synthase - Non-Specific - Mitochondrial proteinAlas-H protein5-Aminolevulinic Acid Synthase 1 proteinDelta-Ala Synthase 1 proteinDelta-Aminolevulinate Synthase 1 proteinALAS1 proteinALAS3 proteinALASH proteinOK proteinSW-cl.121 protein |
Information sourced from Uniprot.org