| Host: | Rabbit |
| Applications: | WB/ELISA |
| Reactivity: | Human |
| Note: | STRICTLY FOR FURTHER SCIENTIFIC RESEARCH USE ONLY (RUO). MUST NOT TO BE USED IN DIAGNOSTIC OR THERAPEUTIC APPLICATIONS. |
| Clonality : | Polyclonal |
| Conjugation: | Unconjugated |
| Isotype: | IgG |
| Formulation: | PBS with 0.02% Sodium Azide, 50% Glycerol, pH 7.3. |
| Purification: | Affinity purification |
| Concentration: | Lot specific |
| Dilution Range: | WB:1:500-1:2000ELISA:Recommended starting concentration is 1 Mu g/mL. Please optimize the concentration based on your specific assay requirements. |
| Storage Instruction: | Store at-20°C for up to 1 year from the date of receipt, and avoid repeat freeze-thaw cycles. |
| Gene Symbol: | GLA |
| Gene ID: | 2717 |
| Uniprot ID: | AGAL_HUMAN |
| Immunogen Region: | 150-429 |
| Specificity: | Recombinant fusion protein containing a sequence corresponding to amino acids 150-429 of human Galactosidase alpha (Galactosidase alpha (GLA) ) (NP_000160.1). |
| Immunogen Sequence: | GYYDIDAQTFADWGVDLLKF DGCYCDSLENLADGYKHMSL ALNRTGRSIVYSCEWPLYMW PFQKPNYTEIRQYCNHWRNF ADIDDSWKSIKSILDWTSFN QERIVDVAGPGGWNDPDMLV IGNFGLSWNQQVTQMALWAI MAAPLFMSNDLRHISPQAKA LLQDKDVIAINQDPLGKQGY QLRQGDNFEVWERPLSGLAW AVAMINRQEIGGPRSYTIAV ASLGKGVACNPACFITQLL |
| Function | Catalyzes the hydrolysis of glycosphingolipids and participates in their degradation in the lysosome. |
| Protein Name | Alpha-Galactosidase AAlpha-D-Galactosidase AAlpha-D-Galactoside GalactohydrolaseGalactosylgalactosylglucosylceramidase GlaMelibiaseAgalsidase |
| Database Links | Reactome: R-HSA-6798695Reactome: R-HSA-9840310 |
| Cellular Localisation | Lysosome |
| Alternative Antibody Names | Anti-Alpha-Galactosidase A antibodyAnti-Alpha-D-Galactosidase A antibodyAnti-Alpha-D-Galactoside Galactohydrolase antibodyAnti-Galactosylgalactosylglucosylceramidase Gla antibodyAnti-Melibiase antibodyAnti-Agalsidase antibodyAnti-GLA antibody |
Information sourced from Uniprot.org