| Function | Carboxyltransferase subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism. |
| Protein Name | Methylcrotonoyl-Coa Carboxylase Beta Chain - MitochondrialMccase Subunit Beta3-Methylcrotonyl-Coa Carboxylase 23-Methylcrotonyl-Coa Carboxylase Non-Biotin-Containing Subunit3-Methylcrotonyl-Coa -Carbon Dioxide Ligase Subunit Beta |
| Database Links | Reactome: R-HSA-196780Reactome: R-HSA-3371599Reactome: R-HSA-70895Reactome: R-HSA-9909438 |
| Cellular Localisation | Mitochondrion Matrix |
| Alternative Antibody Names | Anti-Methylcrotonoyl-Coa Carboxylase Beta Chain - Mitochondrial antibodyAnti-Mccase Subunit Beta antibodyAnti-3-Methylcrotonyl-Coa Carboxylase 2 antibodyAnti-3-Methylcrotonyl-Coa Carboxylase Non-Biotin-Containing Subunit antibodyAnti-3-Methylcrotonyl-Coa -Carbon Dioxide Ligase Subunit Beta antibodyAnti-MCCC2 antibodyAnti-MCCB antibody |
Information sourced from Uniprot.org