| Post Translational Modifications | Acetylated. |
| Function | Biotin-attachment subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism. |
| Protein Name | Methylcrotonoyl-Coa Carboxylase Subunit Alpha - MitochondrialMccase Subunit Alpha3-Methylcrotonyl-Coa Carboxylase 13-Methylcrotonyl-Coa Carboxylase Biotin-Containing Subunit3-Methylcrotonyl-Coa -Carbon Dioxide Ligase Subunit Alpha |
| Database Links | Reactome: R-HSA-196780Reactome: R-HSA-3371599Reactome: R-HSA-70895 |
| Cellular Localisation | Mitochondrion Matrix |
| Alternative Antibody Names | Anti-Methylcrotonoyl-Coa Carboxylase Subunit Alpha - Mitochondrial antibodyAnti-Mccase Subunit Alpha antibodyAnti-3-Methylcrotonyl-Coa Carboxylase 1 antibodyAnti-3-Methylcrotonyl-Coa Carboxylase Biotin-Containing Subunit antibodyAnti-3-Methylcrotonyl-Coa -Carbon Dioxide Ligase Subunit Alpha antibodyAnti-MCCC1 antibodyAnti-MCCA antibody |
Information sourced from Uniprot.org