Anti-HJV/Hemojuvelin antibody [SAA1409] {PerCP} (STJA0030580)

SPECIFICATIONS
ClonalityMonoclonal
HostMouse
ConjugationPerCP
IsotypeIgG2ak
STJA0030580-100
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General Information

Short DescriptionMouse monoclonal Hemojuvelin antibody for use in FC in human and rat samples. Datasheet included with dilution recommendations, and related reagents.
ApplicationsFC
HostMouse
ReactivityHuman/Rat
NoteSTRICTLY FOR FURTHER SCIENTIFIC RESEARCH USE ONLY (RUO). MUST NOT BE USED IN DIAGNOSTIC OR THERAPEUTIC APPLICATIONS.

Product Properties

ClonalityMonoclonal
Clone IDSAA1409
IsotypeIgG2ak
ConjugationPerCP
Concentration0.5 mg/mL
PurificationPurified
FormulationPBS pH 7.4, 50% glycerol, 0.05% proclin300
Storage InstructionStore at 4°C for 12 months. Protect from light. Do not freeze.

Target Information

Gene SymbolHJV
Gene ID148738
Uniprot IDRGMC_HUMAN

Additional Info

Post Translational Modifications Autocatalytically cleaved at low pH.the two chains remain linked via two disulfide bonds. Also proteolytically processed by TMPRSS6, several fragments being released in the extracellular space.regulates HJV activity in BMP signaling and thefore iron homeostasis.
Function Acts as a bone morphogenetic protein (BMP) coreceptor. Through enhancement of BMP signaling regulates hepcidin (HAMP) expression and regulates iron homeostasis.
Protein Name Hemojuvelin
Hemochromatosis Type 2 Protein
Hemojuvelin Bmp Coreceptor
Rgm Domain Family Member C
Database Links Reactome: R-HSA-373752
Cellular Localisation Cell Membrane
Lipid-Anchor
Gpi-Anchor
Also Released In The Extracellular Space
Alternative Antibody Names Anti-Hemojuvelin antibody
Anti-Hemochromatosis Type 2 Protein antibody
Anti-Hemojuvelin Bmp Coreceptor antibody
Anti-Rgm Domain Family Member C antibody
Anti-HJV antibody
Anti-HFE2 antibody
Anti-RGMC antibody

Information sourced from Uniprot.org

Citations

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