| Function | Hydrolyzes linear guanidino acids to form urea and the corresponding amines. Displays specificity for substrates having a negatively charged head group and short chains including taurocyamine, guanidino propanoic and butanoic acids. May protect cells by detoxifying potentially harmful amounts of guanidino acids. Metabolizes L-arginine with low efficiency. |
| Protein Name | Guanidino Acid Hydrolase - MitochondrialArginase - MitochondrialGuanidinobutyrase - MitochondrialGuanidinopropionase - Mitochondrial |
| Database Links | Reactome: R-HSA-351143 |
| Cellular Localisation | Mitochondrion |
| Alternative Protein Names | Guanidino Acid Hydrolase - Mitochondrial proteinArginase - Mitochondrial proteinGuanidinobutyrase - Mitochondrial proteinGuanidinopropionase - Mitochondrial proteinAGMAT proteinGDAH protein |
Information sourced from Uniprot.org