| Function | Hydrolyzes linear guanidino acids to form urea and the corresponding amines. Displays specificity for substrates having a negatively charged head group and short chains including taurocyamine, guanidino propanoic and butanoic acids. May protect cells by detoxifying potentially harmful amounts of guanidino acids. Metabolizes L-arginine with low efficiency. | 
  | Protein Name | Guanidino Acid Hydrolase - MitochondrialArginase - MitochondrialGuanidinobutyrase - MitochondrialGuanidinopropionase - Mitochondrial | 
  | Database Links | Reactome: R-HSA-351143 | 
  | Cellular Localisation | Mitochondrion | 
  | Alternative Protein Names | Guanidino Acid Hydrolase - Mitochondrial proteinArginase - Mitochondrial proteinGuanidinobutyrase - Mitochondrial proteinGuanidinopropionase - Mitochondrial proteinAGMAT proteinGDAH protein | 
 
Information sourced from Uniprot.org