Function | Catalyzes the conversion of gamma-aminobutyrate and L-beta-aminoisobutyrate to succinate semialdehyde and methylmalonate semialdehyde, respectively. Can also convert delta-aminovalerate and beta-alanine. |
Protein Name | 4-Aminobutyrate Aminotransferase - Mitochondrial(S-3-Amino-2-Methylpropionate TransaminaseGaba AminotransferaseGaba-AtGamma-Amino-N-Butyrate TransaminaseGaba TransaminaseGaba-TL-Aibat |
Database Links | Reactome: R-HSA-916853 |
Cellular Localisation | Mitochondrion Matrix |
Alternative Protein Names | 4-Aminobutyrate Aminotransferase - Mitochondrial protein(S-3-Amino-2-Methylpropionate Transaminase proteinGaba Aminotransferase proteinGaba-At proteinGamma-Amino-N-Butyrate Transaminase proteinGaba Transaminase proteinGaba-T proteinL-Aibat proteinABAT proteinGABAT protein |
Information sourced from Uniprot.org